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  • aspartylglycosamine amide hydrolase, deficiency
    Aspartylglycosamine amide hydrolase°áÇÌ(¡­ÌÀù¹)
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  • aspartylglycosamine amide hydrolase, deficiency
    Aspartylglycosamine amide hydrolase°áÇÌ(¡­ÌÀù¹)
  • aspartylglycosaminuria
    Aspartylglycosaminuria
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NAAG N-Acetyl Aspartyl Glutamate
AHA acetohydroxamic acid; acquired hemolytic anemia; acute hemolytic anemia; American Heart Association;...
ANA acetylneuraminic acid; American Narcolepsy Association; American Neurological Association; American ...
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AspRS Aspartyl-tRNA synthetase
Naaga N acetyl-aspartyl glutamic acid
NAAG N-Acetyl-aspartyl-glutamate
SAP secreted aspartyl proteinase
CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 6 ÆäÀÌÁö: 1
aspartyl The aminoacyl radical of aspartic acid.
(05 Mar 2000)
aspartylglucosylaminase <enzyme> An enzyme that catalyses the conversion of n(4)-(beta-n-acetyl-d-glucosaminyl)-l-asparagine and water to n-acetyl-beta-d-glucosaminylamine and l-aspartate. It acts only on asparagine oligosaccharides containing one amino acid, i.e. The asparagine has free alpha-amino and alpha-carboxyl groups.
Chemical name: N(4)-(beta-N-Acetyl-D-glucosaminyl)-L-asparagine amidohydrolase
Registry number: EC 3.5.1.26
(12 Dec 1998)
aspartylglycosamine Generic term for compounds of asparagine and a 2-amino sugar; e.g., beta-aspartyl(acetylglucosamine).
(05 Mar 2000)
aspartylglycosaminidase A hydrolytic enzyme that cleaves off L-aspartate from aspartylglycosamines. A deficiency of aspartylglycosaminidase can result in aspartylglycosaminuria.
(05 Mar 2000)
aspartylglycosaminuria One of the disorders of glycoprotein catabolism resulting from the absence of aspartylglycosamine amidohydrolase, characterised by aspartylglycosamine in the urine and spinal fluid. Symptoms develop in the first months of life, with recurrent infections and diarrhoea. Mental retardation, coarse facial features, and skeletal abnormalities are evident by adolescence.
(05 Mar 2000)
aspartyllysine peptidase <enzyme> From human intestinal brush border; stabilised by zn+2
Registry number: EC 3.4.13.-
Synonym: zn-stable aspartyllysine peptidase
(26 Jun 1999)
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beta-aspartyl(acetylglucosamine) Misnomer for 1-(beta-asparagino)-N-acetylglucosamine or 1-(beta-aspartamido)-N-acetylglucosamine, or, formally, 1-(beta-l-aspartamido)-N-2-acetamido-1,2-dideoxy-beta-d-glucose; a compound of N-acetylglucosamine and asparagine, linked via the amide nitrogen of the latter and carbon-1 of the former. An important structural linkage in many glycoproteins.
(05 Mar 2000)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 1 ÆäÀÌÁö: 1
  • Aspartylglucosylaminase - »õâ An enzyme that catalyzes the conversion of N(4)-(beta-N-acetyl-D-glucosaminyl)-L-asparagine and water to N-acetyl-beta-D-glucosaminylamine and L-aspartate. It acts only on asparagine oligosaccharides containing one amino acid, i.e. the asparagine has free alpha-amino and alpha-carboxyl groups. (From Enzyme Nomenclature, 1992) EC 3.5.1.26.
    Synonyms : Aspartylglucosamine Amidohydrolase, Glycosylasparaginase, Amidohydrolase, Aspartylglucosamine, Amidohydrolase, Aspartylglycosamine, Deaspartylase, Aspartylglucosylamine
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aspartyl the acyl radical of aspartic acid.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
aspartylglucosamine N-acetylglucosamine in N-glycosidic linkage with the amino group of asparagine; it is an intermediate in the degradation of glycoproteins and accumulates abnormally in aspartylglycosaminuria.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
aspartylglucosaminidase a lysosomal enzyme of the hydrolase class that catalyzes the cleavage of N-glycosidic linkages between N-acetylglucosamine and asparagine in glycoproteins, a step in the degradation of glycoproteins. Deficiency of the enzyme, an autosomal recessive trait, causes aspartylglycosaminuria. In EC nomenclature, called N4-β-N-acetylglucosaminyl-L--asparaginase.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
aspartylglucosaminuria aspartylglycosaminuria.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
aspartylglycosaminidase N4-β-N-acetylglucosaminyl-L-asparaginase; see aspartylglucosaminidase.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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