| arylsulfatase B |
Lysosomal enzyme deficient in MPS VI.
출처: www.mpssociety.org/lib-glossary.html
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|---|---|
| aryl- |
any organic group derived from an aromatic hydrocarbon by the removal of a hydrogen atom, for example (C6H5- {phenyl radical, from benzene}).
출처: www.tef.marmara.edu.tr/makine/gurcan/enerji/indust...
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| aryl |
any organic group derived from an aromatic hydrocarbon by the removal of a hydrogen atom, for example (C6H5- {phenyl radical, from benzene}).
출처: www.tef.marmara.edu.tr/makine/gurcan/enerji/indust...
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| arylsulfatase A |
The lack of this enzyme results in the toxic accumulation of sulfatide deposits in metachromatic leukodystrophy, leading to demyelination of the CNS.
출처: www.myelin.org/glossary.htm
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| arylsulfatase B |
The enzyme, or tiny cellular machine, that people with MPS VI don't have enough of. The enzyme works within the lysosomes of every cell to break down and recycle a specific kind of material
출처: www.maroteaux-lamy.com/pc/about/Glossary.asp
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