| adrenoleukodystrophy |
An inherited metabolic disorder in which the myelin sheath on nerve fibres is lost and the adrenal gland degenerates, which leads to progressive neurological disability and death. People with adrenoleukodystrophy accumulate high levels of very-long-chain fatty acids in their brain and adrenal cortex, because the fatty acids are not broken down in a normal manner.
출처: www.nature.com/nrm/journal/v6/n3/glossary/nrm1591_...
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| adrenoleukodystrophy |
A genetic, X-linked condition in which the body over-produces very long-chain saturated fatty acids (20- to 28-carbon chains) that destroy the myelin which is the insulation of nerves in the central nervous system. The disease is usually fatal in childhood, but its effects can be slowed down with a mixture of 20% erucic acid and 80% oleic acid (Lorenzos oil). Aerobic
출처: www.findhealer.com/glossary/A.php3
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| adrenoleukodystrophy |
A rapidly progressive X-linked genetic disorder marked by the accumulation of saturated very long chain fatty acids (VLCFA) in all tissues and body fluids, with a preference for the brain and the adrenal glands. This buildup leads to inflammation of the brain and erosion of the white matter of the central nervous system and the adrenal glands. It affects only boys; while there is a neonatal form, it typically strikes between the ages of 6 and 10.
출처: www.myelin.org/glossary.htm
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