| Rendu-Osler-Weber syndrome | <gastroenterology> An inherited disease characterised by thin blood vessel walls in the nose, skin and gastrointestinal tract. This condition ins associated with a high risk of bleeding complications. Inheritance: autosomal dominant. (27 Sep 1997) |
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| Weber-Cockayne syndrome | <syndrome> This represents a group of rare inherited disorders in which blistering of the skin occurs in response to skin trauma. Large fluid-filled blisters can occur in response to injury, skin rubbing, chafing or even increases in room temperature. Secondary bacterial infection of the blisters is common. Complications include oesophageal stricture, infections, loss of function of hands and feet and malnutrition. The dermatologist is the expert in the evaluation and treatment of this disorder. (27 Sep 1997) |
| Weber's syndrome | <syndrome> Midbrain tegmentum lesion characterised by ipsilateral oculomotor nerve paresis and contralateral paralysis of the extremities, face, and tongue. Synonym: Weber's sign. (05 Mar 2000) |
| Sturge-Kalischer-Weber syndrome | <syndrome> A congenital syndrome consisting of nevus flammeus of the face, haemangiomas of the leptomeninges and choroid, and late glaucoma. It is often associated with intracranial calcification, mental retardation, contralateral hemiplegia, and epilepsy. (12 Dec 1998) |
| sturge-weber-dimitri syndrome | <radiology> Encephalotrigeminal angiomatosis, leptomeningeal capillary-venous angiomatosis, with subjacent cortical calcification, ipsilateral port-wine stains (venous angioma) of face, ipsilateral congenital glaucoma, contralateral focal sz (90%) and hemiparesis (33-66%), subnormal mentation (50%) (12 Dec 1998) |
| sturge-weber syndrome | <syndrome> A congenital syndrome consisting of nevus flammeus of the face, haemangiomas of the leptomeninges and choroid, and late glaucoma. It is often associated with intracranial calcification, mental retardation, contralateral hemiplegia, and epilepsy. (12 Dec 1998) |
| syndrome, klippel-trenaunay-weber | A congenital malformation syndrome characterised by the triad of asymmetric limb hypertrophy, haemangiomata, and nevi. Asymmetric limb hypertrophy is enlargement of one limb and not the corresponding limb on the other side, the enlarged limb being 3 times more likely to be a leg than an arm in ktw; and the limb enlargement is of bone as well as soft tissue. The haemangiomas, abnormal nests of blood vessels that proliferate inappropriately and excessively, cover a remarkable range from small innocuous capillary haemangiomas ( strawberry marks ) to huge cavernous haemangiomas. The nevi are pigmented moles on the skin; in ktw there are often also dark linear streaks on the skin, streaks due to too much pigment. There can be other abnormalities but the triad is the consistent clinical centrepiece of the disease. most persons with ktw have an enlarged leg and do relatively well without treatment or, for example, with only compression from an elastic stocking. Skin ulcers and other skin problems can occur over the swollen leg. Usually, the treatment is conservative. Surgery is almost never needed. The only possible exceptions are the very rare situations in which the leg reaches gigantic proportions or secondary clotting difficulties arise (due to trapping and destruction of blood platelets in a huge haemangioma). Then, amputation may become necessary. The cause of ktw syndrome is unknown. (12 Dec 1998) |
| Klippel-Trenaunay-Weber syndrome | <syndrome> A congenital malformation syndrome characterised by the triad of asymmetric limb hypertrophy, haemangiomata, and nevi. Asymmetric limb hypertrophy is enlargement of one limb and not the corresponding limb on the other side, the enlarged limb being 3 times more likely to be a leg than an arm in ktw; and the limb enlargement is of bone as well as soft tissue. The haemangiomas, abnormal nests of blood vessels that proliferate inappropriately and excessively, cover a remarkable range from small innocuous capillary haemangiomas ( strawberry marks ) to huge cavernous haemangiomas. The nevi are pigmented moles on the skin; in ktw there are often also dark linear streaks on the skin, streaks due to too much pigment. There can be other abnormalities but the triad is the consistent clinical centrepiece of the disease. most persons with ktw have an enlarged leg and do relatively well without treatment or, for example, with only compression from an elastic stocking. Skin ulcers and other skin problems can occur over the swollen leg. Usually, the treatment is conservative. Surgery is almost never needed. The only possible exceptions are the very rare situations in which the leg reaches gigantic proportions or secondary clotting difficulties arise (due to trapping and destruction of blood platelets in a huge haemangioma). Then, amputation may become necessary. The cause of ktw syndrome is unknown. (12 Dec 1998) |
| weber | <physics> The standard unit of electrical quantity, and also of current. See Coulomb, and Ampre. Origin: From the name of Professor Weber, a German electrician. Source: Websters Dictionary (01 Mar 1998) |
| Weber-Christian disease | relapsing febrile nodular nonsuppurative panniculitis |
| Weber, Ernst | <person> German physiologist and anatomist, 1795-1878. See: Weber's experiment, Weber's glands, Weber's law, Weber's paradox, Weber's test for hearing, Fechner-Weber law, Weber-Fechner law. (05 Mar 2000) |
| Weber-Fechner law | The intensity of a sensation varies by a series of equal increments (arithmetically) as the strength of the stimulus is increased geometrically; if a series of stimuli is applied and so adjusted in strength that each stimulus causes a just perceptible change in intensity of the sensation, then the strength of each stimulus differs from the preceding one by a constant fraction; thus, if a just perceptible change in a visual sensation is produced by the addition of 1 candle to an original illumination of 100 candles, 10 candles will be required to produce any change in sensation when the original illumination was one of 1000 candles. Synonym: Fechner-Weber law, Weber's law. (05 Mar 2000) |
| Weber, Frederick Parkes | <person> English physician, 1863-1962. See: Weber-Christian disease, Weber-Cockayne syndrome, Rendu-Osler-Weber syndrome, Sturge-Kalischer-Weber syndrome, Sturge-Weber disease, Sturge-Weber syndrome, Klippel-Trenaunay-Weber syndrome. (05 Mar 2000) |
| Weber, Moritz | <person> German anatomist, 1795-1875. See: Weber's organ. (05 Mar 2000) |
| Weber's experiment | If the peripheral end of the divided vagus nerve is stimulated the heart is arrested in diastole. (05 Mar 2000) |