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"Pyruvate Dehydrogenase Complex Deficiency Disease"¿¡ ´ëÇÑ ´ëÇÑÀÇÇù ÀÇÇпë¾î ¼¼ºÎ °Ë»ö °á°úÀÔ´Ï´Ù
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú :
15
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ÇѱÛ
pyruvate
ÇÇ·çºê»ê¿°
pyruvate kinase
ÇÇ·çºê»ê¿°Å°³ª¾ÆÁ¦
deficiency disease
°áÇ̺´
fat deficiency disease
Áö¹æ°áÇ̺´
nutritional deficiency disease
¿µ¾ç°áÇ̺´
alcohol dehydrogenase
¾ËÄÚ¿ÃÅ»¼ö¼ÒÈ¿¼Ò
dehydrogenase
Å»¼ö¼ÒÈ¿¼Ò
glucose dehydrogenase
Æ÷µµ´çÅ»¼ö¼ÒÈ¿¼Ò
glucose-6-phosphate dehydrogenase
6-ÀλêÆ÷µµ´çÅ»¼ö¼ÒÈ¿¼Ò
glutamate dehydrogenase
±Û·çŽ»êÅ»¼ö¼ÒÈ¿¼Ò
hydroxybutyrate dehydrogenase
¼ö»êÈºÎÆ¼·¹ÀÌÆ®Å»¼ö¼ÒÈ¿¼Ò
lactate dehydrogenase
Á¥»êÅ»¼ö¼ÒÈ¿¼Ò, LDH
malate dehydrogenase
¸»»êÅ»¼ö¼ÒÈ¿¼Ò
succinic dehydrogenase
¼÷½Å»êÅ»¼ö¼ÒÈ¿¼Ò
immune-complex disease
¸é¿ªº¹ÇÕüº´
´ÙÀ½
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú :
15
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1
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ÇѱÛ
pyruvate
ÇÇ·çºê»ê¿°
iron deficiency anemia
ö°áÇ̺óÇ÷
deficiency
°áÇÌ(Áõ)
dehydrogenase
Å»¼ö¼ÒÈ¿¼Ò
succinic dehydrogenase
¼÷½Å»êÅ»¼ö¼ÒÈ¿¼Ò
complex
º¹ÇÕ, º¹ÇÕü, ÄÞÇ÷º½º
basal complex
¹Ù´Úº¹ÇÕÃþ
Golgi's complex
°ñÁöº¹ÇÕü
inferiority complex
¿µîÄÞÇ÷º½º, ¿µî°¨
junctional complex
ÀÌÀ½ºÎº¹ÇÕü
synaptonemal complex
ÀÌÀ½½Çº¹ÇÕü
atypical complex hyperplasia
ºñÁ¤Çüº¹ÇÕÀڱ󻸷Áõ½Ä
complex hyperplasia
º¹ÇÕÁõ½ÄÁõ
complex partial seizure
º¹ÇպκйßÀÛ
anemia of chronic disease
¸¸¼ºº´ºóÇ÷
´ÙÀ½
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú :
15
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ÇѱÛ
pyruvate kinase
ÇÇ·çºó»ê¿°Å°³ª¾ÆÁ¦
pyruvate
ÇÇ·çºê»ê¿°
deficiency disease
¿µ¾ç°áÇ̺´
fat deficiency disease
Áö¹æ°áÇÌÁõ
nutritional deficiency disease
¿µ¾ç°áÇ̺´
alcohol dehydrogenase
¾ËÄÚ¿ÃÅ»¼ö¼ÒÈ¿¼Ò
dehydrogenase
Å»¼ö¼ÒÈ¿¼Ò
glucose dehydrogenase
Æ÷µµ´çÅ»¼ö¼ÒÈ¿¼Ò
glutamate dehydrogenase
±Û·çŽ»êÅ»¼ö¼ÒÈ¿¼Ò
succinic dehydrogenase
¼÷½Å»êÅ»¼ö¼ÒÈ¿¼Ò
hydroxybutyrate dehydrogenase
¼ö»êÈºÎÆ¼·¹ÀÌÆ®Å»¼ö¼ÒÈ¿¼Ò
lactate dehydrogenase
Á¥»êÅ»¼ö¼ÒÈ¿¼Ò
immune-complex disease
¸é¿ªº¹ÇÕüº´
acid lipase deficiency
»ê¼ºÁöÁúºÐÇØÈ¿¼Ò°áÇÌ
acquired immune deficiency
ÈÄõ¸é¿ª°áÇÌ
´ÙÀ½
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú :
15
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ÇѱÛ
glucose-6-phosphate dehydrogenase deficiency
±Û·çÄÚ½º-6-ÀλêµðÇÏÀÌ µå·ÎÀú³×À̽º °áÇÌ(Áõ)
phosphate dehydrogenase deficiency
Àλ꿰ݼö¼ÒÈ¿¼Ò°áÇÌÁõ
GPT => glutamic pyruvate transaminase
±Û·çŽÇÇ·çºó»êÆ®¶õ½º¾Æ¹Ì³ªÁ¦
glutamate pyruvate transaminase
±Û·çŽÇÇ·çºó»êÆ®¶õ½º¾Æ¹Ì³ªÁ¦
pyruvate
ÇÇ·çºê»ê¿°
pyruvate kinase
ÇÇ·çºê»ê¿° Ű³ªÁ¦
pyruvate pathway
ÇÇ·çºê»ê¿°´ë»ç°æ·Î(¡ß«ç¤ÓÛÞóÌèÖØ).
immune complex disease
¸é¿ªº¹ÇÕüº´.
glucuronidase deficiency disease
±Û·çÅ¥·Î´Ïµ¥À̽º °áÇÌÁõ
immune deficiency disease
¸é¿ª°áÇÌÁúȯ<º´>.
18-dehydrogenase
18-Å»¼ö¼ÒÈ¿¼Ò, 18-µðÇÏÀ̵å·Î°Ô³ªÁ¦
18-hydroxysteroid dehydrogenase
18-È÷µå·Ï½Ã½ºÅ×·ÎÀ̵åÅ»¼ö¼ÒÈ¿¼Ò
3-beta-hydroxysteroid dehydrogenase
3-º£Å¸-È÷µå·Ï½Ã½ºÅ×·ÎÀ̵å Å»¼ö¼ÒÈ¿¼Ò
6-P-gluconate dehydrogenase
6-ÆÄ¶ó-±Û·çÄÚ³×ÀÌÆ®Å»¼ö¼ÒÈ¿¼Ò<--µðÇÏÀ̵å·Î°Ô³ªÁ¦>
6-phosphoglycerate dehydrogenase
6-Æ÷½ºÆ÷±Û¸®¼¼·¹ÀÌÆ®Å»¼ö¼ÒÈ¿¼Ò<--µðÇÏÀ̵å·Î°Ô³ªÁ¦>
´ÙÀ½
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú :
15
ÆäÀÌÁö:
1
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ÇѱÛ
glucose-6-phosphate dehydrogenase deficiency
±Û·çÄÚ½º-6-ÀλêµðÇÏÀÌ µå·ÎÀú³×À̽º °áÇÌ(Áõ)
phosphate dehydrogenase deficiency
Àλ꿰ݼö¼ÒÈ¿¼Ò°áÇÌÁõ
glutamate pyruvate transaminase
±Û·çŽÇÇ·çºó»êÆ®¶õ½º¾Æ¹Ì³ªÁ¦
pyruvate
ÇÇ·çºê»ê¿°
pyruvate kinase
ÇÇ·çºê»ê¿° Ű³ªÁ¦
pyruvate pathway
ÇÇ·çºê»ê¿°´ë»ç°æ·Î(¡ß«ç¤ÓÛÞóÌèÖØ).
father complex See complex
ºÎ¼ºÄÞÇ÷º½º(Ý«àõ~)
factor viii-vwf complex deficiency
Á¦8-vWF º¹ÇÕ °áÇÇ
immune complex disease
¸é¿ªº¹ÇÕüº´.
tubular immune complex disease
°ü»ó¸é¿ªº¹ÇÕüº´
acyl-coa dehydrogenase
acyl-CoA Å»¼ö¼ÒÈ¿¼Ò(¡÷â©áÈý£áÈ)
alcohol dehydrogenase
¾ËÄڿõðÇÏÀ̵å·ÎÀú³×À̽º.
alcohol dehydrogenase
¾ËÄÚ¿ÃÅ»¼ö¼ÒÈ¿¼Ò
dehydrogenase
µðÇÏÀ̵å·ÎÀú³×À̽º, Å»¼ö¼ÒÈ¿¼Ò.
dehydrogenase
Å»¼ö¼ÒÈ¿¼Ò(÷â©áÈý£áÈ)
´ÙÀ½
ÀÌ ¾Æ·¡ ºÎÅÍ´Â °á°ú°¡ ¾ø½À´Ï´Ù.
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0
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1
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ÇѱÛ
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0
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1
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ÇѱÛ
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö ¸ÂÃã °Ë»ö °á°ú :
0
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0
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¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö ¸ÂÃã °Ë»ö °á°ú :
0
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ÅëÇÕ°Ë»ö ¿Ï·á
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