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  • N-acetylgalactosamine
    N-¾Æ¼¼Æ¿°¥¶ôÅä»ç¹Î
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N-acetylgalactosamine-1-phosphate kinase <enzyme> Catalyses phosphorylation of n-acetylgalactosamine to form n-acetylgalactosamine-1-phosphate
Registry number: EC 2.7.1.-
Synonym: galnac-1-phosphate kinase, galnac-alpha-1p kinase
(26 Jun 1999)
N-acetylgalactosamine-4-sulfotransferase <enzyme> Present in the pituitary and other tissues, account for the synthesis of glycoproteins bearing oligosaccharides terminating with galnac-4-so4
Registry number: EC 2.8.2.-
Synonym: galnac-4-sulfotransferase
(26 Jun 1999)
N-acetylgalactosamine-6-sulfatase <enzyme> Defective in mucopolysaccharidosis iva (morquio a)
Registry number: EC 3.1.6.4
Synonym: n-acetylgalactosamine-6-sulfate sulfatase
(26 Jun 1999)
N-acetylgalactosamine-mucin alpha-N-1,3-N-acetylgalactosaminyltransferase <enzyme> Forms sia-alpha2-6(gal-nac-alpha1-3)galnac-mucin
Registry number: EC 2.4.1.-
Synonym: mucin-acetylgalactosaminyltransferase, mucin-gal-nac-transferase
(26 Jun 1999)
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  • N-Acetylgalactosamine-4-Sulfatase - »õâ An arylsulfatase that catalyzes the hydrolysis of the 4-sulfate groups of the N-acetyl-D-galactosamine 4-sulfate units of chondroitin sulfate and dermatan sulfate. A deficiency of this enzyme is responsible for the inherited lysosomal disease, Maroteaux-Lamy syndrome (MUCOPOLYSACCHARIDOSIS VI). EC 3.1.6.12.
    Synonyms : Arylsulfatase B1, Arylsulfatase B2, N-Acetylgalactosamine 4-Sulfatase, N-Acetylgalactosamine-4-sulfate Sulfatase, N-Acetylgalactosamine-4-sulphate Sulphatase, 4-Sulfatase, N-Acetylgalactosamine, B, Arylsulfatase, B1, Arylsulfatase, B2, Arylsulfatase
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