| methionine synthase |
The MTR gene provides instructions for making an enzyme called methionine synthase reductase (MTRR), a mitochondrial precursor. This enzyme activates cobalamin-dependent methionine synthase. Methionine synthase is involved in processing amino acids (the building blocks of proteins). Specifically, it carries out a chemical reaction that converts the amino acid homocysteine to another amino acid, methionine. Methionine is used by the body to make proteins and other important compounds.
출처: www.thoughtfulhouse.org/0405-conf-glossary.htm
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| methionine |
1. chemical name: α-amino-γ-methylmercaptobutyric acid; a naturally occurring essential amino acid furnishing both methyl groups and sulfur necessary for normal metabolism. See also table at amino acid. 2. [USP] a preparation of methionine used as a dietary supplement.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| methionine adenosyltransferase |
[EC 2.5.1.6] an enzyme of the transferase class that catalyzes the formation of S-adenosylmethionine from methionine and ATP, occurring in several isozymes. Deficiency of the hepatic isozyme causes hypermethioninemia, but is otherwise benign.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| methionine malabsorption s. |
an autosomal recessive disorder of methionine absorption in which the urine has a characteristic odor resembling that of the interior of an oasthouse (room where tobacco, hops, and malt are dried). It is due to alpha-hydroxybutyric acid formed by bacterial action on the unabsorbed methionine. Characteristics include white hair, mental retardation, convulsions, and attacks of hyperpnea. Called also oasthouse urine disease and Smith-Strang disease.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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