| Ramsay Hunt's syndrome | <syndrome> An intention tremor beginning in one extremity, gradually increasing in intensity, and subsequently involving other parts of the body. Synonym: progressive cerebellar tremor. Facial paralysis, otalgia, and herpes zoster resulting from viral infection of the seventh cranial nerve and geniculate ganglion, a form of juvenile paralysis agitans associated with primary atrophy of the pallidal system. Synonym: paleostriatal syndrome, pallidal syndrome. Synonym: Ramsay Hunt's syndrome. (05 Mar 2000) |
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| Hunt's syndrome | <syndrome> An intention tremor beginning in one extremity, gradually increasing in intensity, and subsequently involving other parts of the body. Synonym: progressive cerebellar tremor. Facial paralysis, otalgia, and herpes zoster resulting from viral infection of the seventh cranial nerve and geniculate ganglion, a form of juvenile paralysis agitans associated with primary atrophy of the pallidal system. Synonym: paleostriatal syndrome, pallidal syndrome. Synonym: Ramsay Hunt's syndrome. (05 Mar 2000) |
| Tolosa-Hunt syndrome | <syndrome> Cavernous sinus syndrome produced by an idiopathic granuloma. (05 Mar 2000) |
| Ramsay Hunt | See: Hunt. (05 Mar 2000) |
| hunt | 1. To search for or follow after, as game or wild animals; to chase; to pursue for the purpose of catching or killing; to follow with dogs or guns for sport or exercise; as, to hunt a deer. "Like a dog, he hunts in dreams." (Tennyson) 2. To search diligently after; to seek; to pursue; to follow; often with out or up; as, to hunt up the facts; to hunt out evidence. "Evil shall hunt the violent man to overthrow him." (Ps. Cxl. 11) 3. To drive; to chase; with down, from, away, etc.; as, to hunt down a criminal; he was hunted from the parish. 4. To use or manage in the chase, as hounds. "He hunts a pack of dogs." (Addison) 5. To use or traverse in pursuit of game; as, he hunts the woods, or the country. Origin: AS. Huntian to hunt; cf. Hentan to follow, pursue, Goth. Hinan (in comp) to seize. Cf. Hent. Source: Websters Dictionary (01 Mar 1998) |
| Hunt, James Ramsay | <person> U.S. Neurologist, 1872-1937. See: Hunt's atrophy, Hunt's neuralgia, Hunt's paradoxical phenomenon, Hunt's syndrome, Ramsay Hunt's syndrome. (05 Mar 2000) |
| Hunt's atrophy | An obsolete term for atrophy of the small muscles of the hand without sensory disturbances; two types are recognised: thenar, from compression of the thenar branch of the median nerve; hypothenar, from compression of the deep palmar branch of the ulnar nerve. (05 Mar 2000) |
| Hunt's neuralgia | A severe paroxysmal lancinating pain deep in the ear, on the anterior wall of the external meatus, and on a small area just in front of the pinna. Synonym: geniculate otalgia, Hunt's neuralgia, neuralgia facialis vera. (05 Mar 2000) |
| Hunt's paradoxical phenomenon | In dystonia musculorum deformans, if an attempt is made at plantar flexion of the foot when the foot is in dorsal spasm the only response is an increase of the extensor, or dorsal, spasm; if, however, the patient is told to extend the foot which is already in a state of strong dorsal flexion, there will be a sudden movement of plantar flexion; the same phenomenon, mutatis mutandis, is observed when there is a condition of strong plantar flexion. (05 Mar 2000) |
| Hunt, William E | <person> U.S. Neurosurgeon, *1921. See: Tolosa-Hunt syndrome. (05 Mar 2000) |
| Aarskog-Scott syndrome | A syndrome of ocular hypertelorism, anteverted nostrils, broad upper lip, saddle-bag scrotum, and laxity of ligaments resulting in genu recurvatum, flat feet, and hyperextensible fingers; X-linked and autosomal dominant forms. Synonym: Aarskog-Scott syndrome. (05 Mar 2000) |
| Aarskog syndrome | <syndrome> Grier et al. (1983) reported father and 2 sons with typical Aarskog syndrome, including short stature, hypertelorism, and shawl scrotum. They tabulated the findings in 82 previous cases. X-linked recessive inheritance has been repeatedly suggested. The family reported by Welch (1974) had affected males in 3 consecutive generations. Thus, there is either genetic heterogeneity or this is an autosomal dominant with strong sex-influence and possibly ascertainment bias resulting from use of the shawl scrotum as a main criterion. Stretchable skin was present in the cases of Grier et al. (1983). Teebi et al. (1993) reported the case of an affected mother and 4 sons (including a pair of monozygotic twins) by 2 different husbands. They suggested that the manifestations were as severe in the mother as in the sons and that this suggested autosomal dominant inheritance. Actually, the mother seemed less severely affected, compatible with X-linked inheritance. Clinical signs: Mild to moderate short stature,normocephaly, Widow's peak hair, maxillary hypoplasia, broad nasal bridge, anteverted nostrils, long philtrum, broad upper lip, curved linear dimple below the lower lip, hypertelorism, ptosis, down-slanted palpebral fissures, ophthalmoplegia, strabismus, hyperopic astigmatism, large cornea, floppy ears, lop-ears,cleft lip/palate, shawl scrotum, saddle-bag scrotum, cryptorchidism, brachydactyly, digital contractures, clinodactyly, mild syndactyly, transverse palmar crease, lymphoedema of the feet, ligamentous laxity, osteochondritis dissecans, proximal finger joint hyperextensibility, flexed distal finger joints, genu recurvatum, flat feet, stretchable skin, cervical spine hypermobility, odontoid anomaly, macrocytic anaemia, hemochromatosis, hepatomegaly, portal cirrhosis, imperforate anus, rectoperineal fistula, interstitial pulmonary disease, sternal deformity. Inheritance: Sex-influenced autosomal dominant form, also X-linked form. (05 Aug 1998) |
| abdominal muscle deficiency syndrome | <syndrome> Congenital absence (partial or complete) of abdominal muscles, in which the outline of the intestines is visible through the protruding abdominal wall; in males, genitourinary anomalies (urinary tract dilation and cryptorchidism) are also found; genetics unclear. (05 Mar 2000) |
| abstinence syndrome | <syndrome> A constellation of physiologic changes undergone by persons or animals who have become physically dependent on a drug or chemical due to prolonged use at elevated doses, but who are abruptly deprived of that substance. The abstinence syndrome varies with the drug to which dependence has developed. Generally the effects observed are in an opposite direction from those produced by the drug; e.g., the withdrawal syndrome from central nervous system depressants such as barbiturates and benzodiazepines consists of insomnia, restlessness, tremulousness, hallucinations, and, in the extreme, tonic-clonic convulsions which may prove fatal. The onset time and severity of the abstinence syndrome depend upon how rapidly the drug disappears from the body. (05 Mar 2000) |
| Achard syndrome | <syndrome> Arachnodactyly with small receding mandible, broad skull, and joint laxity limited to the hands and feet; genetics unclear. (05 Mar 2000) |