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  • Beckwith¡¯s syndrome
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  • beckwith-wiedemann syndrome
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BWS battered woman (or wife) syndrome; Beckwith-Wiedemann syndrome
WBS Wechsler-Bellevue Scale; whole-blood serum; whole-body scan; Wiedemann-Beckwith syndrome; withdrawal...
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BWS Beckwith Wiedemann Syndrome
WBS Wiedemann Beckwith syndrome
CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 3 ÆäÀÌÁö: 1
Beckwith syndrome <syndrome> This syndrome, of unknown cause, is characterised by a group of the following findings: large tongue, organ enlargement (visceromegaly), large body size, umbilical hernia and neonatal hypoglycaemia. Evidence suggests a genetic lesion. Birth weight is often more than 8 pounds. Complications include Wilm's tumour, seizures, aspiration and hypoglycaemia.
(27 Sep 1997)
Beckwith, John Beckwith <person> U.S. Pathologist, *1933.
See: Beckwith-Wiedemann syndrome.
(05 Mar 2000)
Beckwith-Wiedemann syndrome <syndrome> This syndrome, of unknown cause, is characterised by a group of the following findings: large tongue, organ enlargement (visceromegaly), large body size, umbilical hernia and neonatal hypoglycaemia. Evidence suggests a genetic lesion. Birth weight is often more than 8 pounds. Complications include Wilm's tumour, seizures, aspiration and hypoglycaemia.
(27 Sep 1997)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 1 ÆäÀÌÁö: 1
  • Beckwith-Wiedemann Syndrome - »õâ A syndrome of multiple defects characterized primarily by umbilical hernia (HERNIA, UMBILICAL); MACROGLOSSIA; and GIGANTISM; and secondarily by visceromegaly; HYPOGLYCEMIA; and ear abnormalities.
    Synonyms : Wiedemann-Beckwith Syndrome, Beckwith Wiedemann Syndrome, Exomphalos Macroglossia Gigantism Syndrome, Syndrome, Beckwith-Wiedemann, Syndrome, Exomphalos-Macroglossia-Gigantism, Syndrome, Wiedemann-Beckwith, Wiedemann Beckwith Syndrome
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  • Beckwith-Wiedemann syndrome - »õâ
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Beckwith-Wiedemann syndrome A rare, overgrowth disorder in which babies are large at birth and may develop low blood sugar. Other common symptoms are a large tongue, large internal organs, and defects of the abdominal wall near the navel. Beckwith-Wiedemann syndrome increases the risk of developing certain cancers, especially Wilms' tumor.
Ãâó: www.stjude.org/glossary
Beckwith's s. a congenital autosomal dominant syndrome with variable expressivity characterized by exomphalos, macroglossia, and gigantism, often associated with visceromegaly, adrenocortical cytomegaly, and dysplasia of the renal medulla. Called also EMG s. and exomphalos-macroglossia-gigantism s.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
Beckwith's syndrome Beckwith-Wiedemann syndrome; see under syndrome.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
Beckwith-Wiedeman syndrome An autosomal dominant syndrome whose hallmarks are enlargement of the tongue and visceral organs, gigantism, and umbilical hernia, often with neonatal hypoglycemia.
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