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"tuberous sclerosis"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
À̰ÍÀ» ¿øÇϼ̽À´Ï±î?
¾Ë±â½¬¿î ÀÇÇпë¾îÇ®ÀÌÁý, ¼­¿ïÀÇ´ë ±³¼ö ÁöÁ¦±Ù, °í·ÁÀÇÇÐ ÃâÆÇ À¯»ç °Ë»ö °á°ú : 3 ÆäÀÌÁö: 1
¿µ¹® sclerosis ÇÑ±Û °æÈ­(Áõ), ±»À½(Áõ)
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¿µ¹® amyotrophic laternal sclerosis ÇÑ±Û ±ÙÀ§ÃàÃø»è°æÈ­Áß
¼³¸í   
  »ç¶÷ÀÌ ±ÙÀ° Çϳª¸¦ ¿òÁ÷À϶§ »ç¿ëÇϴ ½Å°æ¿¬°áÀ» »ìÆìº¸¸é ´ÙÀ½°ú °°´Ù. ¿ì¼± ´ë³ú¿¡ Àִ ¿îµ¿À» °üÀåÇϴ °÷ÀΠ¿îµ¿°ÑÁú¿¡¼­ÀÇ ¸í·ÉÀÌ ¶³¾îÁö¸é À̰ÍÀº Ã´¼ö¸¦ Å¸°í °è¼ÓÇØ¼­ ³»·Á¿À°Ô µÈ´Ù. ±×¸®°í Ã´¼ö¿¡¼­ Çѹø ½Å°æ¼¼Æ÷¸¦ ¹Ù²Ù¾î¼­ ¸»ÃʽŰ栱ÙÀ°¿¡ °¡¼­ ±ÙÀ°À» ¿òÁ÷ÀδÙ. Áï ´ë³ú¿¡¼­ ¶³¾îÁø ¸í·ÉÀÌ ½Å°æ¼¼Æ÷ Çϳª¸¦ Å¸°í Ã´¼ö±îÁö °¡°í Ã´¼ö¿¡¼­ ÇÑ ¹ø ½Å°æÀ» ¹Ù²Ù¾î ±ÙÀ°À¸·Î °£´Ù.
  
  Ã´¼ö¿¡¼­ ½ÃÀÛÇÏ¿© ±ÙÀ°±îÁö °¡´Â ½Å°æ ¼¼Æ÷¸¦ ¾Õ»Ô¼¼Æ÷¶ó°í ÇÑ´Ù. ¿øÀΠ¹Ì»óÀΠÀÌ º´Àº ¾Õ»Ô¼¼Æ÷ÀÇ ¼Ò½Ç¿¡ ÀÇÇØ¼­ ±×°ÍÀÇ Áö¹è¸¦ ¹Þ´Â ±ÙÀ°ÀÇ À§ÃàÀÌ ³ªÅ¸³ª´Â °ÍÀ» ÁÖÁõ»óÀ¸·Î ÇÑ´Ù. ÀÌ º´¿¡ Æ¯È¿°¡ Àִ ġ·á¹ýÀº ¾ÆÁ÷ ¾ø´Ù.
¿µ¹® multiple sclerosis ÇÑ±Û ´Ù¹ß°æÈ­Áõ
¼³¸í   
  ½Å°æÃà»èÀ» µÑ·¯½Î°í Àִ ¸»ÀÌÁý(myelin sheath)ÀÇ ÆÄ±«·Î ÀÎÇÑ º´Àû»óŸ¦ ¸»ÇÔ. ÆÄ±«µÈ ¸»ÀÌÁýÀº ÈäÅ͸¦ ³²±â°Ô µÇ¾î ½Å°æÃà»èÀ» ÅëÇÑ ½Å°æÀü´ÞÀÌ Á¦´ë·Î µÇÁö ¾Ê¾Æ ¿îµ¿, °¨°¢, ÀÚÀ²½Å°æ ¸ðµÎÀÇ ½Å°æÀü´ÞÀå¾Ö°¡ ³ªÅ¸³­´Ù. ÀÌ º´Åʹ ¾îµð¼­³ª ³ªÅ¸³¯ ¼ö À־ ±× Àå¾Ö°¡ ³ªÅ¸³ª´Â ºÎÀ§¿¡ µû¶ó ¼­·Î ´Ù¸¥ Áõ»óÀ» È£¼ÒÇÑ´Ù.
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • annular sclerosis
    °í¸®°æÈ­, ȯ»ó°æÈ­
  • areolar choroidal sclerosis
    ¿øÇü¸Æ¶ô¸·°æÈ­(Áõ)
  • arteriolar sclerosis
    ¼¼µ¿¸Æ°æÈ­(Áõ)
  • amyotrophic lateral sclerosis
    ±ÙÀ°À§Ãà°¡ÂʰæÈ­(Áõ), ±ÙÀ§ÃàÃø»è°æÈ­(Áõ)
  • bulbar sclerosis
    ¼û³ú°æÈ­(Áõ), ¿¬¼ö°æÈ­(Áõ)
  • combined sclerosis
    ¿¬ÇÕ°æÈ­Áõ
  • coronary sclerosis
    °ü»óµ¿¸Æ°æÈ­Áõ, ½ÉÀ嵿¸Æ°æÈ­Áõ
  • calcific sclerosis
    ¼®È¸°æÈ­
  • choroidal sclerosis
    ¸Æ¶ô¸·°æÈ­Áõ
  • degenerative diffuse cerebral sclerosis
    ÅðÇ౤¹üÀ§´ë³ú°æÈ­(Áõ)
  • diffuse cerebral sclerosis
    ±¤¹üÀ§´ë³ú°æÈ­Áõ
  • diffuse sclerosis
    ±¤¹üÀ§°æÈ­Áõ
  • diffuse systemic sclerosis
    ±¤¹üÀ§Àü½Å°æÈ­Áõ
  • disseminated sclerosis
    ÆÄÁ¾°æÈ­Áõ
  • endocardial sclerosis
    ½É³»¸·°æÈ­Áõ
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 4 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • sclerosis
    °æÈ­(Áõ), ±»À½(Áõ)
  • amyotrophic lateral sclerosis
    ±ÙÀ°À§Ãà°¡ÂʰæÈ­Áõ
  • multiple sclerosis
    ´Ù¹ß°æÈ­Áõ
  • systemic sclerosis
    Àü½Å°æÈ­Áõ
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • tuberous sclerosis
    °áÀý°æÈ­Áõ
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • tuberous xanthoma
    °áÀýȲ»öÁ¾
  • tuberous xanthomatosis
    °áÀýȲ»öÁ¾Áõ
  • amyotrophic lateral sclerosis
    ±ÙÀ°À§Ãà°¡ÂʰæÈ­Áõ
  • annular sclerosis
    °í¸®°æÈ­Áõ
  • areolar choroidal sclerosis
    ¿øÇü¸Æ¶ô¸·°æÈ­(Áõ)
  • arteriolar sclerosis
    (¢¡arteriolosclerosis) ¼¼µ¿¸Æ°æÈ­Áõ
  • bulbar sclerosis
    ¿¬¼ö°æÈ­Áõ, ¼û³ú°æÈ­Áõ
  • calcific sclerosis
    ¼®È¸°æÈ­Áõ
  • choroidal sclerosis
    ¸Æ¶ô¸·°æÈ­(Áõ)
  • combined sclerosis
    (¢¡subacute combined degeneration) ¾Æ±Þ¼º¿¬ÇÕº¯¼º
  • coronary sclerosis
    ½ÉÀ嵿¸Æ°æÈ­Áõ, °ü»óµ¿¸Æ°æÈ­Áõ
  • degenerative diffuse cerebral sclerosis
    ÅðÇ౤¹üÀ§³ú°æÈ­(Áõ)
  • diffuse sclerosis
    ±¤¹üÀ§°æÈ­Áõ
  • diffuse cerebral sclerosis
    ±¤¹üÀ§³ú°æÈ­Áõ
  • diffuse systemic sclerosis
    ±¤¹üÀ§Àü½Å°æÈ­Áõ
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Bournevilles disease->tuberous sclerosis
    ºÎ¸£³×ºôº´
  • amyotrophic lateral sclerosis
    ±ÙÀ§Ã༺ Ãø»è °æÈ­Áõ(¡­ö°ßãÌãûùñø).
  • amyotrophic lateral sclerosis
    ±ÙÀ§Ãà¼ºÃø»è°æÈ­Áõ(ÐÉê×õêàõö°ÞþÌãûùñø)
  • annular sclerosis
    À±»ó°æÈ­Áõ(¡­Ìãûùñø).
  • anterior spinal sclerosis
    Àü»è°æÈ­Áõ(îñßãÌãûùñø).
  • aortic sclerosis
    ´ëµ¿¸Æ°æÈ­(Áõ)(¡­Ìãûùñø).
  • areolar choroidal sclerosis
    ¿øÇü¸Æ¶ô¸·°æÈ­(Áõ)
  • funicular sclerosis
    »è»ó°æÈ­(Áõ).
  • hepatoportal sclerosis
    °£¹®¸Æ°æÈ­Áõ.
  • hereditary cerebellar sclerosis
    À¯Àü¼º ¼Ò³ú°æÈ­Áõ.
  • hereditary spinal sclerosis
    À¯Àü¼º ô¼ö °æÈ­Áõ(¡­Ìãûùñø).
  • hereditary spinal sclerosis
    À¯Àü¼º ô¼ö°æÈ­Áõ(¡­Ìãûùñø).
  • hodgkins disease,nodular sclerosis
    °áÀý¼º °æÈ­¼º
  • pigmentary sclerosis
    »ö¼Ò°æÈ­Áõ(ßäáÈàõ)
  • posterior spinal sclerosis
    ÈÄô¼ö°æÈ­Áõ (¡­Ìãûùñø).
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö ¸ÂÃã °Ë»ö °á°ú : 3 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • tuberous sclerosis
    °áÀý¼º°æÈ­Áõ
  • tuberous sclerosis
    °áÀý¼º °æÈ­Áõ
  • tuberous sclerosis
    °áÀý¼º °æÈ­Áõ.
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • tuberous tumor
    °áÀý¼º Á¾¾ç(¡­ðþåË)
  • tuberous xanthoma
    °áÀý¼º Ȳ»öÁ¾
  • tuberous xanthomatosis
    °áÀý¼º Ȳ»öÁ¾Áõ(Ì¿ï½àõüÜßäðþñø)
  • amyotrophic lateral sclerosis
    ±ÙÀ§Ã༺ Ãø»è °æÈ­Áõ(¡­ö°ßãÌãûùñø).
  • amyotrophic lateral sclerosis
    ±ÙÀ§Ãà¼ºÃø»è°æÈ­Áõ(ÐÉê×õêàõö°ÞþÌãûùñø)
  • annular sclerosis
    À±»ó°æÈ­Áõ(¡­Ìãûùñø).
  • anterior spinal sclerosis
    Àü»è°æÈ­Áõ(îñßãÌãûùñø).
  • aortic sclerosis
    ´ëµ¿¸Æ°æÈ­(Áõ)(¡­Ìãûùñø).
  • areolar choroidal sclerosis
    ¿øÇü¸Æ¶ô¸·°æÈ­(Áõ)
  • arteriolar sclerosis
    ¼¼µ¿¸Æ¼º °æÈ­Áõ.
  • bulbar sclerosis
    ±¸<¿¬¼ö>°æÈ­Áõ(Ϲ<æÅâÐ>Ìãûùñø).
  • calcific sclerosis
    ¼®È¸¼º°æÈ­Áõ(à´üéàõÌãûùñø).
  • calcific sclerosis
    ¼®È¸È­°æÈ­Áõ(¡­Ìãûùñø)
  • cardiac sclerosis
    ½ÉÀμº °æÈ­Áõ (ãýì×àõÌãûùñø)
  • cardiac sclerosis,hepatic
    °£ °æÈ­Áõ(ÊÜÌãûùñø)
´ëÇѽŰæ¿Ü°úÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
    ÇÑÀÚ
  • tuberous sclerosis
    °áÀý°æÈ­Áõ
    Ì¿ï½àõÌãûùñø
KI ÀÇÇпë¾î »çÀü °Ë»ö ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • tuberous sclerosis
    °áÀý¼º°æÈ­Áõ
KI ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 3 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • amyotrophic lateral sclerosis
    ±ÙÀ§Ãà¼ºÃø»è°æÈ­Áõ
  • multiple sclerosis
    ´Ù¹ß¼º°æÈ­Áõ
  • posterolateral sclerosis
    ÈÄ»èÃø»è°æÈ­Áõ
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
TSC technetium sulfur colloid; thiosemicarbazide; transverse spinal sclerosis; tuberous sclerosis
ALS acute lateral sclerosis; advanced life support; afferent loop syndrome; amyotrophic lateral sclerosi...
TS   1) Tricuspid Stenosis
  2) Tuberous Sclerosis
    = ...
TS Takayasu syndrome; Tay-Sachs; temperature sensitivity; temperature, skin; temporal stem; tensile str...
NS natural science; Neosporin; nephrosclerosis; nephrotic syndrome; nervous system; neurological surger...
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
TS Tuberous Sclerosis
TSc Tuberous Sclerosis
Tsc2 Tuberous sclerosis 2
TSC Tuberous sclerosis complex
TSC2 tuberous sclerosis gene
Çѱ¹Ç¥ÁØÁúº´»çÀκзù ¾àÀÚ ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
  • ÄÚµå
    ¿µ¹®
    ÇѱÛ
  • Q85.1
    Tuberous sclerosis
    °áÀý¼º °æÈ­Áõ
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü ¸ÂÃã °Ë»ö °á°ú : 2 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • tuberous sclerosis
    °áÀý¼º °æÈ­Áõ
    »ó¿°»öü ¿ì¼º À¯ÀüÀ» ÇÏ´Â º¹ÇÕÀûÀÎ ½Å°æ ÇǺΠÁõÈıºÀ¸·Î °£Áú, Á¤½Å ¹Ú¾à ¹× Ç÷°ü ¼¶À¯Á¾°ú »þ±×¸° ¹Ý
  • tuberous sclerosis
    °áÀý¼º °æÈ­Áõ
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • tuberous
    °áÀý¼º
  • amyotrophic lateral sclerosis
    ±ÙÀ§Ã༺ Ãø»è °æÈ­Áõ, ±ÙÀ§Ã༺ Ãø¹æ °æÈ­
    1. Ãßü·ÎÀÇ ´º·Ð ¹× ³ú°£°ú ô¼öÀÇ ¿îµ¿¼¼Æ÷ÀÇ ÁøÇ༺ÀÎ º¯¼ºÀ» Ư¡À¸·Î ÇÏ´Â ÁúȯÀ¸·Î¼­, »óÀ§ ¹× ÇÏÀ§ÀÇ ¿îµ¿½Å°æÀÇ °á¼ÕÀ» ÃÊ·¡ÇÑ´Ù. º¸Åë 2-3³â³»¿¡ »ç¸ÁÇÑ´Ù. 2. »óÀ§ 1Â÷ ¿îµ¿ ´º·Ð°ú ÇÏÀ§ 2Â÷ ¿îµ¿ ´º·ÐÀÌ ÇÔ²² ħ¹üµÇ´Â ¿øÀÎ ºÒ¸íÀÇ °èÅ뼺 ÁúȯÀ¸·Î 30-50¼¼ÀÇ ³²¼º¿¡°Ô ¸¹´Ù. Áö°¢Àå¾Ö´Â ¾ø´Ù. ´ë°³ ¼Õ ±ÙÀ°ÀÇ ±Ù·Â ÀúÇÏ¿Í À§ÃàÀÌ µÇ¸é¼­ Â÷Ãû ÁøÇàÇÏ¿© ÆÈ, ¾î±úÀÇ ±ÙÀ°¿¡ ¹ÌÄ£´Ù. ´õ ³ª¾Æ°¡ ÇÏÁöÀÇ ±ÙÀ°ÀÌ À§ÃàÇϰųª, ±¸À½, ¿¬Çϱٵµ ħ¹üµÇ¾î ±¸¸¶ºñ Áõ»óÀ» ³ªÅ¸³½´Ù. ½ÉºÎ¹Ý»ç´Â Åë»ó Ç×ÁøÇÏ°í ±ÙÀ°¿¡´Â ¼¶À¯¼º ¿¬ÃàÀ» º¸°Ô µÈ´Ù. ƯȿÀûÀÎ Ä¡·á¹ýÀº ¾ø°í ¿¹Èİ¡ ºÒ·®ÇÏ¸ç Æò±Õ 3³â, ´ëºÎºÐ 5³â À̳»¿¡ »ç¸ÁÇÑ´Ù.
  • annular sclerosis
    À±»ó °æÈ­Áõ
    ôÃß ÁÖÀ§¿¡ ´ë»óÀ¸·Î »ý±â´Â °æÈ­Áõ.
  • areolar choroidal sclerosis
    ¿øÇü ¸Æ¶ô¸· °æÈ­
  • condylar sclerosis
    °úµÎ °æÈ­Áõ
  • dentinal sclerosis
    »ó¾Æ ¼¼°ü °æ»ö, »ó¾ÆÁú °æÈ­Áõ
    Àڱؿ¡ ´ëÇÑ »ó¾ÆÁúÀÇ ¹ÝÀÀÀ¸·Î¼­ »ó¾Æ¼¼°üÀÇ Á¡Â÷ÀûÀÎ ¼®È¸È­¸¦ ¸»ÇÑ´Ù. ÀÌ´Â ¿ì½Ä, ±³¸ðÁõ, ¶Ç´Â Ä¡°æºÎ ¸¶¸ðÁõ¿¡ ÀÇÇØ »ó¾ÆÁúÀÌ ±¸°­ ȯ°æ¿¡ ¸¸¼ºÀûÀ¸·Î ³ëÃâµÇ´Â °æ¿ì ¹ß»ýµÇ¸ç ³ëÃâµÈ »ó¾ÆÁúÀº À¯¸®¿Í °°ÀÌ ¹Ý¦À̴ ǥ¸é Áú°¨À» °®°í ÀÖ´Ù. ÇÑÆí, »ó¾ÆÁú¿¡ ´ëÇÑ ¿­Àû, È­ÇÐÀû, Ã˰¢ÀûÀÎ Àڱؿ¡ ´ëÇØ Ä¡¼ö¸¦ È¿°úÀûÀ¸·Î º¸È£ÇÏ´Â ÀÛ¿ëÀ» Áö´Ï°í ÀÖ´Ù.
  • diffuse sclerosis
    ¹ü¹ß¼º °æÈ­Áõ
  • lichen sclerosis et atrophicus
    °æÈ­ À§Ã༺ ÆíÆò ż±
    ¸¸¼º À§Ã༺ÀÇ ÇǺΠÁúȯÀ¸·Î, ºÎÁ¤ÇüÀÇ ÆíÆòÇÑ ±¸ÁøÀÌ °¢Àü°ú ÇÔ¿ä¿¡ ÀÇÇÏ¿© ´ÙÇü¼ºÀ» ³ªÅ¸³»´Â °ÍÀÌ Æ¯Â¡ÀÌ´Ù. ³²ÀÚ´Â À½°æ¿¡ ¹ß»ýÇÏ´Â Æó»ö¼º °ÇÁ¶¼º ±ÍµÎ¿°°ú ¿©ÀÚÀÇ ¿ÜÀ½ºÎ¿¡ ¹ßº´ÇÏ´Â ¿ÜÀ½ À§Ãà ÁõÀÇ °¡Àå ÈçÇÑ ¿øÀÎÀÌ µÈ´Ù.
  • muscle sclerosis
    ±Ù °æÈ­Áõ
  • posterolateral sclerosis syndrome
    ÈÄ»è Ãø»è °æÈ­Áõ ÁõÈıº
  • primary lateral sclerosis
    ¿ø¹ß¼º Ãø»ö °æÈ­Áõ
  • progressive systemic sclerosis
    ÁøÇ༺ Àü½Å °æÈ­Áõ, ÁøÇ༺ Àü½Å¼º °æÈ­Áõ, ÁøÇ༺ Àü½Å¼º °øÇÇÁõ
  • pulmonary sclerosis
    Æó °æÈ­Áõ
  • pulp sclerosis
    Ä¡¼ö ¼®È¸Áõ
    Ä¡¼ö°­°ú Ä¡±Ù°ü¿¡¼­ ¹ß»ýµÇ´Â ¶Ç ´Ù¸¥ ÇüÅÂÀÇ ¼®È¸È­ Çö»óÀÌ´Ù. Ä¡¼ö¼®°ú´Â ´Þ¸® Ä¡¼ö ¼®È¸ÁõÀº ´õ¿í ±¤¹üÀ§ÇÑ ÇüÅÂÀÌ´Ù. ¿øÀÎÀº Àß ¾Ë·ÁÁ® ÀÖÁö ¾ÊÀ¸³ª ¿¬·É°ú Å« °ü°è°¡ ÀÖ´Â °Í °°´Ù. 10-20¼¼ÀÇ ¸ðµç Ä¡¾Æ Áß 60%, 50-70¼¼ÀÇ ¸ðµç Ä¡¾Æ Áß 90%°¡ Á¶Á÷ÇÐÀûÀ¸·Î Ä¡¼ö ¼®È¸ÁõÀÇ ¼Ò°ßÀ» º¸¿´°í Á¶Á÷ÇÐÀûÀ¸·Î ¼®È¸È­ÀÇ ÇüÅ´ ¹«Á¤ÇüÀÌ°í ¹«±¸Á¶¸¦ º¸ÀÌÁö¸¸ Ä¡¼ö¿¡ ÀÖ´Â Ç÷°ü°ú ½Å°æ¿¡ ÆòÇàÇÑ ´ë»ó
  • sclerosis
    °æÈ­, °æÈ­Áõ, °ñ °æÈ­Áõ, °æ°á, °æÈ­
    ƯÈ÷ ¿°Áõ ¹× °£Áú Áúȯ¿¡ ÀÇÇØ¼­ »ý±â´Â ºÎºÐÀû °æÈ­·Î¼­, ÀÌ ¿ë¾î´Â ÁÖ·Î °áÇÕ Á¶Á÷ÀÇ °úÇü¼º¿¡ ÀÇÇÑ ½Å°æ°èÀÇ °æÈ­ ¶Ç´Â Ç÷°üÀÇ °æÈ­¿¡ ´ëÇØ¼­ »ç¿ëµÈ´Ù.
CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
tuberous sclerosis <radiology> (Bourneville disease) autosomal dominant phakomatosis classic triad: seizures, retardation, adenoma sebaceum, calcified subependymal hamartomas, uncalcified tubers in cerebral cortex, enhancing lesion most likely to be malignant transformation to giant cell astrocytoma associated with: skin lesions, angiomyolipoma, increased risk of renal cell carcinoma
(12 Dec 1998)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
skin lesions of tuberous sclerosis <radiology> Adenoma sebaceum, Shagreen patches, periungual fibromata, ash-leaf hypopigmentation
(12 Dec 1998)
tuberous <botany> Swollen, of roots, tuber-like.
(09 Oct 1997)
tuberous root A root that is swollen for food storage; tuberous primary root's occur in aconite, beet, and carrot; tuberous secondary root's occur in plants of the Umbelliferae; and tuberous adventitious roots occur in jalap and sweet potato.
(05 Mar 2000)
Alzheimer's sclerosis Hyaline degeneration of the medium and smaller blood vessels of the brain.
(05 Mar 2000)
amyotrophic lateral sclerosis A serious neurologic disease that results from the progressive degeneration of the motor neurons.
(27 Sep 1997)
amyotropic lateral sclerosis A chronic progressive disease of motor neurons (the nerves that come from the spinal cord to supply electrical energy to the muscles).
(12 Dec 1998)
arterial sclerosis <cardiology, disease> Imprecise term for various disorders of arteries, particularly hardening due to fibrosis or calcium deposition, often used as a synonym for atherosclerosis.
(17 Oct 1997)
arteriocapillary sclerosis Arteriosclerosis, especially of the finer vessels.
(05 Mar 2000)
arteriolar sclerosis <cardiology, disease> Sclerosis and thickening of the walls of the smaller arteries (arterioles). Hyaline arteriolosclerosis, in which there is homogeneous pink hyaline thickening of the arteriolar walls, is associated with benign nephrosclerosis.
Hyperplastic arteriolosclerosis, in which there is a concentric thickening with progressive narrowing of the lumina may be associated with malignant hypertension, nephrosclerosis and scleroderma.
(17 Oct 1997)
bone sclerosis <medicine> A condition of bone cartilage occurring in certain diseases of these tissues, in which they acquire an unnatural density, and come to resemble ivory.
Origin: L. Eburnus of ivory, fr. Ebur ivory: cf. F. Eburnation. See Ivory.
Source: Websters Dictionary
(01 Mar 1998)
Canavan's sclerosis Autosomal recessive degenerative disease of infancy; mostly in Jewish infants; onset typically within first 3-4 months of birth, consisting of blindness, psychomotor regression, enlarged head, optic atrophy, hypotonia, spasticity, increased N-acetylaspartic acid urinary excretion. MRI shows enlarged brain, decreased attenuation of cerebral and cerebellar white matter, and normal ventricles. Pathologically, there is increased brain volume and weight, and spongy degeneration in the subcortical white matter.
See: leukodystrophy.
Synonym: Canavan's sclerosis, Canavan-van Bogaert-Bertrand disease, spongy degeneration of infancy.
(05 Mar 2000)
valvular sclerosis Fibrosis, often with calcification of valves, considered to be an aging change and not due to primary valvular disease.
(05 Mar 2000)
vascular sclerosis <cardiology, disease> Imprecise term for various disorders of arteries, particularly hardening due to fibrosis or calcium deposition, often used as a synonym for atherosclerosis.
(17 Oct 1997)
mantle sclerosis A common cerebral lesion in the palsied states of early life characterised by nodular cortical atrophy.
(05 Mar 2000)
glomerular sclerosis Hyaline deposits or scarring within the renal glomeruli, a degenerative process occurring in association with renal arteriosclerosis or diabetes.
Synonym: glomerular sclerosis.
Origin: Glomerulus + G. Sklerosis, hardness
(05 Mar 2000)
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  • Tuberous Sclerosis - »õâ An autosomal dominant disorder which is generally classified as a phacomatosis. Pathologically, the condition is characterized by glial cell tumors which arise in the cerebral hemispheres and retina. There is an increased incidence of benign rhabdomyomas of the heart and angiomyolipomas of kidney, liver, lungs, thyroid, and testes. Clinical manifestations include MENTAL RETARDATION; adenoma sebaceum of the face (actually angiofibromas); EPILEPSY; SPASMS, INFANTILE; Shagreen patches on the trunk; and subungual fibromas. (From Adams et al., Principles of Neurology, 6th ed, p1011)
    Synonyms : Bourneville's Disease, Phacomatosis, Bourneville, Bourneville Phacomatosis, Bourneville Phakomatosis, Epiloias, Sclerosis, Tuberous
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tuberous sclerosis Tuberous sclerosis, (meaning "hard potatoes") is a rare genetic, disorder primarily characterized by a triad of seizures, mental retardation, and skin lesions (called adenoma sebaceum). This "classic" Vogt triad is present in 30-50% of cases; in particular, up to 30% of tuberous sclerosis reportedly have normal mentation. ...
Ãâó: en.wikipedia.org/wiki/Tuberous_sclerosis
tuberous sclerosis A genetic disorder in which benign (noncancerous) tumors form in the kidneys, brain, eyes, heart, lungs, and skin. This disease can cause seizures, mental disabilities, and different types of skin lesions.
Ãâó: www.stjude.org/glossary
tuberous sclerosis a genetic disorder of the skin and nervous system characterized by epilepsy, mental retardation, and a skin condition resembling acne
Ãâó: www.american-depot.com/services/resources_gl_t.asp
tuberous sclerosis Also known as Bourneville
Ãâó: www.vh.org/adult/patient/cancercenter/prevention/p...
tuberous sclerosis Rare genetic neurological disorder characterized by seizures, mental retardation, and skin/ eye lesions. There my be tumors in the eyes, and visual functioning can vary depending on the size and severity of the tumors. There may be decreased visual acuity, retinal scarring, retinal detachment, myopic, field loss, or glaucoma.
Ãâó: www.sparkle.usu.edu/glossary/syndromes_glossary.as...
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