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RDD Rosai Dorfman disease
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Rosai-Dorman disease A chronic disease occurring in children and characterised by massive painless cervical lymphadenopathy due to distension of the lymphatic sinuses by macrophages containing ingested lymphocytes, and by capsular and pericapsular fibrosis.
Synonym: Rosai-Dorman disease.
(05 Mar 2000)
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Rosai-Dorfman d. a rare syndrome, seen usually in children or adolescents, in which cervical lymph nodes (and sometimes other lymph nodes) are massively swollen and contain large numbers of histiocytes; extranodal disease is common, sometimes with fever, anemia, neutrophilia, elevated erythrocyte sedimentation rate, and hypergammaglobulinemia. Called also sinus histiocytosis with massive lymphadenopathy.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
Rosai-Dorfman disease see under disease.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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