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  • Phosphofructokinase-1 - »õâ An allosteric enzyme that regulates glycolysis by catalyzing the transfer of a phosphate group from ATP to fructose-6-phosphate to yield fructose-1,6-bisphosphate. D-tagatose- 6-phosphate and sedoheptulose-7-phosphate also are acceptors. UTP, CTP, and ITP also are donors. In human phosphofructokinase-1, three types of subunits have been identified. They are PHOSPHOFRUCTOKINASE-1, MUSCLE TYPE; PHOSPHOFRUCTOKINASE-1, LIVER TYPE; and PHOSPHOFRUCTOKINASE-1, C TYPE; found in platelets, brain, and other tissues.
    Synonyms : 6-Phosphofructo-1-kinase, Fructose-6-P 1-Kinase, Fructose-6-phosphate 1-Phosphotransferase, 6 Phosphofructokinase, Phosphofructokinase 1
  • Phosphofructokinase-1, Liver Type - »õâ An allosteric enzyme that regulates glycolysis by catalyzing the transfer of a phosphate group from ATP to fructose-6-phosphate to yield fructose-1,6-bisphosphate. In human liver, the 6-phosphofructose-1-kinase exists as the homotetramer of L subunits.
    Synonyms : Phosphofructo-1-kinase Isozyme B, Phosphofructokinase 1, Liver Type
  • Phosphofructokinase-1, Muscle Type - »õâ An allosteric enzyme that regulates glycolysis by catalyzing the transfer of a phosphate group from ATP to fructose-6-phosphate to yield fructose-1,6-bisphosphate. In humans, PHOSPHOFRUCTOKINASE-1 in muscle exists as the homotetramer of M subunits. Defects in this muscle enzyme cause GLYCOGEN STORAGE DISEASE TYPE VII, also known as Tarui's disease.
    Synonyms : Phosphofructo-1-kinase Isozyme A, Phosphofructokinase 1, Muscle Type
  • Phosphofructokinase-1, Type C - »õâ An allosteric enzyme that regulates glycolysis by catalyzing the transfer of a phosphate group from ATP to fructose-6-phosphate to yield fructose-1,6-bisphosphate. In the humans, 6-phosphofructose-1-kinase isozyme C is found in platelets, brain, heart, kidney, colon and testis. This isozyme C can exist as the homotetramer of C subunits (P subunits), or heterotetramer of C type and L type subunits.
    Synonyms : Phosphofructo-1-kinase Isozyme C, Phosphofructokinase 1, Type C
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