| long-chain 3-hydroxyacyl CoA dehydrogenase | <enzyme> Deficiency may cause some cases of hypoglycaemic 3-hydroxydicarboxylic aciduria Registry number: EC 1.1.1.211 Synonym: l-chad (26 Jun 1999) |
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| long-chain-acyl-CoA dehydrogenase | <enzyme> Flavoprotein; forms with another flavoprotein plus EC 1.5.5.1 a system reducing ubiquinone and other acceptors Registry number: EC 1.3.99.- Synonym: lc-acyl-CoA dehydrogenase, long-chain-acyl-coenzyme a dehydrogenase, very-long-chain acyl-CoA dehydrogenase, vlcad (26 Jun 1999) |
| long-chain-alcohol dehydrogenase | <enzyme> Catalyses reversibly the oxidation of a long-chain alcohol in the presence of nad to a long-chain acid anion and NADH Registry number: EC 1.1.1.192 Synonym: fatty alcohol-nad+ oxidoreductase (26 Jun 1999) |
| long-chain-alcohol O-fatty-acyltransferase | <enzyme> Catalyses the final step in biosynthesizing storage liquid waxes from long chain fatty acyl CoA and fatty alcohols; forming predominantly c42 wax esters Registry number: EC 2.3.1.75 Synonym: acyl-coenzyme a-alcohol transacylase, aca transacylase, acyl-CoA-alcohol transacylase, wax-ester synthase (26 Jun 1999) |
| long-chain-fatty-acid-(acyl-carrier-protein) ligase | <enzyme> Fatty acid, acyl-carrier-protein-sh and ATP gives acyl-(acyl-carrier-protein), AMP and ppi Registry number: EC 6.2.1.20 Synonym: fatty acid-acyl carrier protein ligase (AMP), acyl-(acyl-carrier-protein)synthetase, aacp synthetase, fatty acyl-acyl carrier protein synthase, vibrio harveyi, acyl-(acyl-carrier-protein) synthetase, acyl-acp synthetase (26 Jun 1999) |
| long-chain-fatty-acid-CoA ligase | <enzyme> Fatty acid thiokinase (long-chain), a ligase forming acyl-CoA, AMP, and pyrophosphate from long-chain fatty acids, ATP, and coenzyme A. Activity is independent of phosphatidylcholine Registry number: EC 6.2.1.3 Synonym: acyl-activating enzyme, dodecanoyl-CoA synthetase, fatty acid thiokinase (long chain), acid-coenzyme a ligase, fatty acid-CoA ligase, acyl-CoA synthetase, acyl-CoA ligase, coash ligase, ciprofibroyl-CoA synthetase, pristanoyl-CoA synthetase, palmityl CoA synthetase, palmitoyl CoA synthetase, palmitoyl CoA ligase, fatty acyl-CoA synthetase, very long chain fatty acid acyl-CoA synthetase, vlcfa acyl-CoA synthetase, nafenopin-CoA ligase, palmitoyl-CoA synthase, faa2 gene product, faa2p protein, vlacs enzyme (26 Jun 1999) |
| long-chain-fatty-acyl-glutamate deacylase | <enzyme> Lca aminoacylase I almost specific to l-glutamate-containing lipoamino acids; lca aminoacylase II acts on fatty acyl amino acids with chain lengths between c11 and c16 Registry number: EC 3.5.1.55 Synonym: lca aminoacylase I, lca aminoacylase II, n-long chain acyl aminoacylase (26 Jun 1999) |
| long-chain a. (LCAD) deficiency |
a defect in mitochondrial beta oxidation due to deficiency of the acyl-CoA dehydrogenase acting on long chain length fatty acids. It is clinically similar to MCAD deficiency, but urinary excretion is of long-chain dicarboxylic acids and skeletal muscle weakness and cardiac enlargement may also be present.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| long-chain-fatty-acid–CoA ligase |
[EC 6.2.1.3] an enzyme of the ligase class that catalyzes the formation of acyl coenzyme A from long chain fatty acids (12 or more carbons) and coenzyme A, using energy derived from ATP hydrolysis. The enzyme occurs in the mitochondrial outer membrane, endoplasmic reticulum, and peroxisome membrane, and it acts on saturated and unsaturated fatty acids as well as some hydroxy acids. Called also acyl CoA synthetase.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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