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IPH Idiopathic pulmonary haemosiderosis
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haemosiderosis Conditions in which there is a generalised increase in the iron stores of body tissues, particularly of liver and the reticuloendothelial system, without demonstrable tissue damage. The name refers to the presence of stainable iron in the tissue in the form of haemosiderin.
(12 Dec 1998)
haemosiderosis / haemochromatosis <radiology> Iron deposition due to abnormal metabolism or iron overload, primary abnormal iron metabolism, secondary alcoholic cirrhosis, multiple blood transfusions (e.g., Hb SS, thalassaemia) Findings: osteoporosis, chondrocalcinosis (calcium pyrophosphate deposition disease), arthropathy, resembles calcium pyrophosphate deposition disease arthropathy, distinctive feature: BEAK-like osteophytes at MCP jts, mottled increased density of liver and spleen, Definitions: haemosiderosis: haemosiderin deposition within cells, haemochromatosis: haemosiderin within cells AND interstitium
(12 Dec 1998)
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pulmonary haemosiderosis Haemosiderosis usually associated with mitral stenosis and marked by an accumulation of macrophages loaded with haemosiderin within the alveoli.
(05 Mar 2000)
nutritional haemosiderosis A disease seen in black South Africans that results from ingestion of iron in foodstuffs prepared in iron vessels; excessive absorption of iron affects the liver.
(05 Mar 2000)
idiopathic pulmonary haemosiderosis <chest medicine> A rare, sporadic, fatal, mostly in children with an equal sex distribution.
The condition also occurs in adults where there is a sex difference (M:F = 2:1). The patients present with recurrent attacks of pulmonary haemorrhage, acute phase: bat-wing alveolar infiltrates, clears rapidly, chronic findings: haemosiderosis, pulmonary fibrosis, cor pulmonale.
(12 Dec 1998)
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haemosiderosis abnormal deposit of hemosiderin
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