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ADPase adenosine diphosphatase
DDase deoxyuridine diphosphatase
FDPase fructose-1,6-diphosphatase
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ADPase Adenosine diphosphatase
FDPase Fructose-1,6-diphosphatase
NDP-ase Nucleoside diphosphatase
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ATP-diphosphatase <enzyme> An enzyme that catalyses breakdown of ATP to AMP, usually extracted from plants, but aortic and placental forms have also been described.
(18 Nov 1997)
fructose-1,6-diphosphatase deficiency An autosomal recessive fructose metabolism disorder due to absent or deficient fructose-1,6-diphosphatase activity. Gluconeogenesis is impaired, resulting in accumulation of gluconeogenic precursors (e.g., amino acids, lactate, ketones) and manifested as hypoglycaemia, ketosis, and lactic acidosis. Episodes in the newborn infant are often lethal. Later episodes are often brought on by fasting and febrile infections. As patients age through early childhood, tolerance to fasting improves and development becomes normal.
(12 Dec 1998)
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