| PORP | partial ossicular replacement prosthesis |
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| PORP | Partial Ossicular Replacement Prosthesis |
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| 영문 | porphyria | 한글 | 포르피린증 |
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| 설명 | 포르피린 또는 그 전구물질의 형성이나 배설의 현저한 증가를 특징으로 하는 포르피린 대사장애에 대한 총칭. 네 개의 피롤핵이 메틸기로 연결된 포피린유도체의 총칭이다. 측쇄에 메틸기, 에틸기, 비닐기, 프로피온산기 등이 들어간 유로포피린, 코프로포피린, 프로토포피린, 헤마토포피린 등이 알려져 있다. 포르피린환에 Fe2+가 들어간 GPA은 글로빈과 결합하여 혈색소를 구성한다. 철포르피린으로서는 헤모글로빈, 시토크롬, 카타라아제 등이 있고, Mg2+를 갖는 것으로서는 엽록소가 있다. 생체조직 중, 주로 골수의 어린 적혈구 그리고 간에서 이루어지는 헴합성의 중간대사물질로, 혈색소나 각종 헴단백의 소재가 된다. 헴합성 이상에 의해 적혈구, 혈장, 소변, 대변의 포르피린체가 증가한다. 헴합성의 이상은 각 형의 포피리아, 빈혈, 납중독 등에서 볼 수 있다. |
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| porphin | <protein> A cyclic tetrapyrrole in which the four pyrrole groups are linked by their alpha-carbon atoms via methene (-CH=) bridges, porphin is the partial compund of porphyrins. (14 Oct 1997) |
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| porphine | The unsubstituted cyclic tetrapyrrole nucleus that is the basis of the porphyrins. See: porphyrins. Compare: chlorin, phorbin, corrin. Synonym: porphyrin. (05 Mar 2000) |
| porphobilin | General term denoting intermediates between the monopyrrole, porphobilinogen, and the cyclic tetrapyrrole of haem (a porphin derivative). See: bilin. (05 Mar 2000) |
| porphobilinogen | <chemical> Chemical name: 1H-Pyrrole-3-propanoic acid, 5-(aminomethyl)-4-(carboxymethyl)- (12 Dec 1998) |
| porphobilinogen oxygenase | <enzyme> Porphobilinogen is converted to 5-oxo-porphobilinogen Registry number: EC 1.13.- (26 Jun 1999) |
| porphobilinogen synthase | <enzyme> An enzyme that catalyses the formation of porphobilinogen from two molecules of 5-aminolevulinic acid. Chemical name: 5-Aminolevulinate hydro-lyase (adding 5-aminolevulinate and cyclizing) Registry number: EC 4.2.1.24 (12 Dec 1998) |
| porphobilinogen synthase porphyria | An inherited disorder in which there is a deficiency of porphobilinogen synthase; d-aminolevulinate levels are elevated, leading to neurological disturbances. Synonym: porphobilinogen synthase porphyria. (05 Mar 2000) |
| porphobilinogenase | <enzyme> A combination of uroporphyrinogen I synthase and uroporphyrinogen isomerase which catalyses the formation of uroporphyrinogen III from porphobilinogen; minor descriptor (75-84); on-line and index medicus search ammonia-lyases (75-84) Registry number: EC 5.- (26 Jun 1999) |
| porphyria | A pathological state in man and some lower animals that is often due to genetic factors, is characterised by abnormalities of porphyrin metabolism and results in the excretion of large quantities of porphyrins in the urine and in extreme sensitivity to light. (18 Nov 1997) |
| porphyria cutanea tarda | A form of hepatic porphyria (porphyria, hepatic) characterised by photosensitivity resulting in bullae that rupture easily to form shallow ulcers. This condition occurs in two forms: a sporadic, nonfamilial form that begins in middle age and has normal amounts of uroporphyrinogen decarboxylase with diminished activity in the liver; and a familial form in which there is an autosomal dominant inherited deficiency of uroporphyrinogen decarboxylase in the liver and red blood cells. (12 Dec 1998) |
| porphyria cutanea tarda hereditaria | A form of hepatic porphyria (porphyria, hepatic) characterised by photosensitivity resulting in bullae that rupture easily to form shallow ulcers. This condition occurs in two forms: a sporadic, nonfamilial form that begins in middle age and has normal amounts of uroporphyrinogen decarboxylase with diminished activity in the liver; and a familial form in which there is an autosomal dominant inherited deficiency of uroporphyrinogen decarboxylase in the liver and red blood cells. (12 Dec 1998) |
| porphyria cutanea tarda symptomatica | A form of hepatic porphyria (porphyria, hepatic) characterised by photosensitivity resulting in bullae that rupture easily to form shallow ulcers. This condition occurs in two forms: a sporadic, nonfamilial form that begins in middle age and has normal amounts of uroporphyrinogen decarboxylase with diminished activity in the liver; and a familial form in which there is an autosomal dominant inherited deficiency of uroporphyrinogen decarboxylase in the liver and red blood cells. (12 Dec 1998) |
| porphyria hepatica | A category of porphyria that includes porphyria cutanea tarda, variegate porphyria, and coproporphyria. Synonym: porphyria hepatica. (05 Mar 2000) |
| porphyria, acute intermittent | A form of hepatic porphyria (porphyria, hepatic) characterised by periodic attacks of gastrointestinal disturbances, abdominal colic, paralyses, and psychiatric disorders. The onset of this condition is usually in the third or fourth decade of life. (12 Dec 1998) |
| porphyria, erythrohepatic | A form of porphyria characterised by a wide range of photocutaneous changes, liver disease, and an excess of protoporphyrin. (12 Dec 1998) |
Synonyms :
Synonyms : ALA-Dehydrase, delta-Aminolevulinate Dehydratase, delta-Aminolevulinic Acid Dehydratase, ALA Dehydrase, Acid Dehydratase, Aminolevulinic, Acid Dehydratase, delta-Aminolevulinic, Aminolevulinate Hydro Lyase, Dehydratase, Aminolevulinic Acid
Synonyms :
Synonyms :
Synonyms : Acute Porphyria, Acute Intermittent Porphyria, Acute Intermittent Porphyrias, Acute Porphyrias, Intermittent Porphyria, Acute, Intermittent Porphyrias, Acute, Porphyria, Acute, Porphyrias, Acute, Porphyrias, Acute Intermittent
| porphyria |
a genetic abnormality of metabolism causing abdominal pains and mental confusion
출처: wordnet.princeton.edu/perl/webwn
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| porphyrin |
any of various pigments distributed widely in living tissues
출처: wordnet.princeton.edu/perl/webwn
|
| porphyric polyneuropathy |
a severe, often symmetrical type of polyneuropathy that occurs with some varieties of porphyria.
출처: www.mercksource.com/pp/us/cns/cns_hl_dorlands.jspz...
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| porphyria |
a group of genetic disorders in which substances called porphyrins build up in the blood, often causing rashes brought on by exposure to sunlight and reactions to certain drugs
출처: www.american-depot.com/services/resources_gl_p.asp
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| porphyria cutanea tarda |
Disorder of heme biosynthesis due to a defective liver enzyme (uroporphyrinogen decarboxylase). Symptoms include photosensitivity; hepatic dysfunction; discolored teeth, gums and skin; excessive hair; and psychiatric symptoms that result from porphyrin accumulation in the blood.
출처: www.cdc.gov/hemochromatosis/training/glossary.htm
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| PORP | a genus of protoctista |
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| PORP | a genetic abnormality of metabolism causing abdominal pains and mental confusion |
| PORP | any of various pigments distributed widely in living tissues |
| PORP | Old World purple gallinules |
| PORP | purple gallinule of southern Europe |
| PORP | (of rocks) consisting of porphyry or containing large crystals in a fine groundmass of minerals |
| PORP | any igneous rock with crystals embedded in a finer groundmass of minerals |
| PORP | American purple gallinules |
| PORP | American purple gallinule |
| PORP | any igneous rock with crystals embedded in a finer groundmass of minerals |
| PORP | any of several small gregarious cetacean mammals having a blunt snout and many teeth |
| PORP | a yellow fatty oil obtained from porpoises and used as a fine lubricant |
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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