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cytochrome-c oxidase <enzyme> An enzyme complex of the inner mitochondrial membrane that catalyses the reaction between ferrocytochrome c and oxygen to yield ferricytochrome c and water.
It is associated with the pumping of protons and the resultant phosphorylation of ADP to ATP. The reaction is the terminal event in the electron transport scheme by which oxygen is used for fuel combustion. It is a part of Complex IV of the respiratory chain.
A deficiency of one or more of the polypeptides of this complex results in neuronal loss in brain leading to psychomotor retardation and neurodegenerative disease.
Synonym: cytochrome aa3, indophenol oxidase, indophenolase. Chemical name: Ferricytochrome-c:oxygen oxidoreductase
Registry number: EC 1.9.3.1
(12 Dec 1998)
cytochrome-c peroxidase <enzyme> A haemprotein which catalyses the oxidation of ferrocytochrome c to ferricytochrome c in the presence of hydrogen peroxide.
Chemical name: Ferrocytochrome c:hydrogen-peroxide oxidoreductase
Registry number: EC 1.11.1.5
(12 Dec 1998)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 2 ÆäÀÌÁö: 1
  • Cytochrome-c Oxidase Deficiency - »õâ A disease that results from a congenital defect in ELECTRON TRANSPORT COMPLEX IV. Defects in ELECTRON TRANSPORT COMPLEX IV can be caused by mutations in the SURF1, SCO2, COX10, or SCO1 genes. ELECTRON TRANSPORT COMPLEX IV deficiency caused by mutation in SURF1 manifests itself as LEIGH DISEASE; that caused by mutation in SCO2 as fatal infantile cardioencephalomyopathy; that caused by mutation in COX10 as tubulopathy and leukodystrophy; and that caused by mutation in SCO1 as early-onset hepatic failure and neurologic disorder. (from Online Mendelian Inheritance in Man, http://www.ncbi.nlm.nih.gov/Omim, MIM#220110, May 17, 2001)
    Synonyms : Cytochrome Oxidase Deficiency, Deficiency, Cytochrome-c Oxidase, Cytochrome Oxidase Deficiencies, Cytochrome c Oxidase Deficiency, Cytochrome-c Oxidase Deficiencies, Deficiencies, Cytochrome Oxidase, Deficiencies, Cytochrome-c Oxidase
  • Cytochrome-c Peroxidase - »õâ A hemeprotein which catalyzes the oxidation of ferrocytochrome c to ferricytochrome c in the presence of hydrogen peroxide. EC 1.11.1.5.
    Synonyms : Cytochrome Peroxidase, Cytochrome c-551 Peroxidase, Cytochrome c 551 Peroxidase, Cytochrome c Peroxidase, Peroxidase, Cytochrome, Peroxidase, Cytochrome c-551, Peroxidase, Cytochrome-c
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