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  • alpha1-acid glycoprotein
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KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
alpha1,3GT Alpha1,3-galactosyltransferase
alpha1-ARs Alpha1-adrenergic receptors
alpha1-AR Alpha1-adrenoceptor
AR Alpha1-adrenergic receptors
AR Alpha1-adrenoceptor
CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 6 ÆäÀÌÁö: 1
alpha-1 antichymotrypsin <chemical> Glycoprotein found in alpha(1)-globulin region in human serum. It is an inhibiter of the digestive protease, chymotrypsin and other chymotrypsin-like proteinases in vivo and has cytotoxic killer-cell activity in vitro.
The protein also has a role as an acute-phase protein and is active in the control of immunologic and inflammatory processes, and as a tumour marker. It is a member of the serpin superfamily.
Pharmacological action: serine proteinase inhibitors.
(12 Dec 1998)
alpha-1 antitrypsin <chemical> Plasma glycoprotein member of the serpin superfamily which inhibits trypsin, neutrophil elastase, and other proteolytic enzymes. Commonly referred to as alpha 1-proteinase inhibitor (a1pi), it exists in over 30 different biochemical variant forms known collectively as the pi (protease inhibitor) system.
Hereditary deficiency is associated with pulmonary emphysema.
See: alpha-1 antitrypsin deficiency
Pharmacological action: serine proteinase inhibitors, trypsin inhibitors.
(12 Dec 1998)
alpha-1 antitrypsin deficiency <chest medicine> Deficiency of the protease inhibitor alpha-1 antitrypsin, leads primarily to degradation of elastin of the alveolar walls, as well as other structural proteins of a variety of tissues.
The lack of this protein leads to damage of various organs, but mainly to the lung and liver.
symptoms may become apparent at a very early age or in adulthood, manifesting either as shortness of breath or liver related symptoms (jaundice, fatigue, fluid in the abdomen, mental changes, or gastrointestinal bleeding). There are several options for treatment of the lung disease, including replacement of the missing protein. Treatment of the liver disease is a well-timed liver transplant
(12 Dec 1998)
alpha-1,3-mannosylglycoprotein beta-1,4-N-acetylglucosaminyltransferase <enzyme> Incorporates n-acetyglucosamine as the third branch of complex n-glycosyl-oligosaccharide of hen oviduct
Registry number: EC 2.4.1.145
Synonym: glcnac-transferase iv, n-acetylglucosaminyltransferase iv, udp-glcnac-gngn(glcnac to man alpha1-3)beta 4-n-acetylglucosaminyltransferase iv
(26 Jun 1999)
alpha-1,4-glucan lyase <enzyme> Degrades alpha-1,4-glucan to produce 1,5-anhydrofructose; from seaweeds gracilariopsis lemaneiformis and gracilaria verrucosa; mw 111 kD; amino acid sequence has been determined
Registry number: EC 4.2.2.-
Synonym: alpha-1,4-glucan 4-lyase
(26 Jun 1999)
alpha-1-proteinase deficiency Absence of a serum proteinase inhibitor that may cause nodular non-suppurative panniculitis.
(05 Mar 2000)
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alpha1-2,alpha1-3,alpha1-6-mannosidase <enzyme> From rat liver; releases alpha1-2, alpha1-3, alpha1-6 linked residues from oligosaccharide substrates; end product of reaction is manalpha1-3(manalpha1-6)manbeta1-4glcnac; mw 110 kD; inhibited by edta, zn++ and cu++, swainsonine and 1-deoxymannojirimycin
Registry number: EC 3.2.1.-
Synonym: 2,3,6-alpha-mannosidase
(26 Jun 1999)
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alpha-1,4-glucosidase deficiency glycogen storage disease, type II.
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alpha-1-a antitrypsin A low-molecular-weight glycoprotein that inhibits proteolytic enzymes. Deficiency of this enzyme is associated with early-onset emphysema in some patients and liver disease in others. Replacement therapy for patients with t
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